A mother of five lived for 99 years with a & # 39; totally backwards & # 39; body, doctors have revealed.
Rose Marie Bentley, from Molalla in northwest Oregon, was discovered with situs inversus with levocardia.
This caused her liver, stomach and pancreas to develop on her right side instead of in their normal more & # 39; left & # 39; position.
Ms. Bentley was unaware of her bizarre anatomy, where her condition only came to light after she had donated her body for medical examination.
The mother – who died in October 2017 – is considered the oldest known person with the condition. Doctors say that the chance of survival after childhood is as small as one in 50 million.
Despite the death of most heart failure patients, Mrs. Bentley's family claims to lead a healthy life, with only arthritis and acid reflux.
Rose Marie Bentley (photo) died on October 11, 2017 at the age of 99. She is considered the oldest known person with situs inversus with levocardia, causing her liver, stomach and pancreas to develop on her right side instead of in their normal left position
Ms. Bentley (pictured as a younger woman), born in 1918, was unaware of her bizarre condition and never had health problems that went beyond arthritis and acid reflux. She is one in 50 million with the condition that survives in adulthood and has unusual heart defects
In March last year, medical students came across the condition of mrs. Bentley against after she donated her body to the Oregon Health & Science University (OHSU) donation program.
Cam Walker, assistant professor of anatomy at the University's anatomical service center, said: & I knew something was wrong, but it took us a while to figure out how she was put together.
& # 39; I think the chance of finding another person like her is as small as one in 50 million. I don't think any of us will ever forget it, honestly. & # 39;
WHAT IS SITUS INVERSUS WITH LEVOCARDIA?
Situs inversus is a genetic disorder that occurs when the internal organs are arranged as a & # 39; mirror image & # 39 ;.
It is thought to have an effect on 22,000 people. Singers Enrique Iglesias and Donny Osmond are known to have it.
The condition causes the main abdominal organs – such as the liver, pancreas and spleen – to shift to the right instead of the usual & # 39; left & # 39; position.
Situs inversus alone rarely causes complications, most patients not knowing they have it.
However, problems can occur if the heart is the only organ that develops on the right side of the body, called situs inversus with levocardia.
This can lead to a fetus developing heart defects that can lead to cardiovascular failure later in life.
It is estimated that the chance that a patient with situs inversus with levocardia living in adulthood is as small as one in 50 million.
Patients with situs inversus must wear a medical identification tag to alert medical personnel that their internal organs have been reversed so that they can act accordingly.
For example, by listening to a heartbeat on the right side instead of the left side of the chest.
The medical students were given the task of assessing the hearts of the cadavers.
Those who studied Ms. Bentley soon saw that she was missing her inferior vena cava & # 39; – the large vein that carries low-oxygen blood from the lower part of the body to the heart to absorb oxygen.
After calling about their professors, student Warren Nielsen – who is now in his second year of medicine – said: "That's when the buzz starts.
& # 39; They are like: "Oh, my God, this is completely retarded!".
Upon closer inspection, doctors noted Mrs. Bentley's abdominal organs as a mirror image.
& # 39; Instead of having a left stomach, which is normal, her stomach was on the right & # 39 ;, said Professor Walker CNN.
& # 39; Her liver, which normally occurs mainly on the right, was mainly on the left.
& # 39; Her spleen was on the right instead of her normal appearance on the left. & # 39;
And that was not the end of Mrs. Bentley's anatomical abnormalities.
Her inferior vena cava was not missing, but ran to the left of her vertebrae instead of to the right.
The veins that usually end up in the liver or breast were missing or in an unusual place.
Her right lung only had two lobes instead of three. And the right atrium of her heart was twice the normal size.
Situs inversus with levocardia affects one in 22,000 births, with most patients suffering from life-threatening heart disease.
Only five to fifteen percent of patients live at the age of five, according to the OHSU team.
They estimate that the chance of a patient surviving to adulthood is one in 50 million.
To the right is a diagram of Mrs. Bentley's mirrored belly, with her stomach, spleen, and pancreas all & # 39; from their normal position & # 39; have been & # 39; moved & # 39 ;. The only vital organ that developed in the right place was her heart. The left shows that she only had two lung lobes, instead of the usual three
I WANT TO LIFE ALWAYS: THE POEM INSPIRATION MENS BENTLEY TO KNOW HER BODY
The day will come when my body will lie on a white sheet that is neatly tucked away under four corners of a mattress in a hospital; busy with the living and the dying.
At a certain moment a doctor will determine that my brain is no longer functioning and that my life has stopped for all purposes.
If that happens, don't try to instill artificial life into my body through the use of a machine, and don't call this my deathbed, let it be called the bed of life, and let my body get out to help others lead better lives.
Give my eyes to the man who has never seen a sunrise, a baby's face or love in the eyes of a woman.
Give my heart to a person whose own heart has caused nothing but endless days of pain.
Give my blood to the teenager who was pulled out of the wreck of his car so that he could live to see his grandchildren play.
Give my kidneys to the one who depends on a machine to exist from week to week.
Take my bones, every muscle, every fiber and nerve in my body and find a way to make a lame child walk.
Explore all corners of my brain.
Take my cells, if necessary, and let them grow, so that one day a speechless boy will scream at the crack of a bat and a deaf girl will hear the sound of rain in her window.
Burn what is left of me and scatter the ashes to the wind to make the flowers grow.
If you have to bury something, let it be my mistakes, my weakness and all prejudices against my fellow man.
Give my sins to the devil.
Give my soul to God.
If you happen to want to remember me, do it with a kind act or a good word for someone who needs you.
If you do everything I have asked, I will live forever.
By Robert Test
Mrs. Bentley did not suffer any cardiovascular problems, which the scientists credit for her long life.
When the heart is mirrored & # 39; & # 39; like the rest of the abdominal organs, a patient is usually fine.
But when the heart is the only organ that does not change its position, as in the case of Mrs. Bentley, the fetus in question typically develops defects that lead to heart failure later in life.
Prior to Mrs. Bentley, only two cases were known where patients lived in their seventies.
Speaking of the investigation, Mr. Nielsen, then 26, said: & # 39; It was pretty amazing.
& # 39; We could not only learn the normal anatomy, but also all the anatomical variations that can occur.
& # 39; I started to appreciate how she could live as long as she did. I wondered who she was.
I look forward to caring for patients and being able to apply what I have learned from her. & # 39;
A poster about Mrs. Bentley's condition was presented at the annual meeting of the American Association of Anatomists 2018 in Experimental Biology in Orlando.
She and her husband James – who died 13 years earlier from pneumonia – decided to donate their bodies to OHSU after reading a moving poem about remembering our loved ones at their death.
I Will Live Forever by Robert Test reads: & # 39; Give my eyes to the man who has never seen a sunrise, a baby & # 39; s face or love in the eyes of a woman.
& # 39; Give my blood to the teenager who has been pulled out of the wreck of his car so that he can live to see his grandchildren play.
& # 39; Give my kidneys to the one who depends on a machine to exist from week to week. & # 39;
It closes with the line: & # 39; If you do everything I have asked, I will live forever. & # 39;
Their family read the same poem during OHSU & # 39; s Service of Gratitude in December 2018, thanking donors and their families for their unselfish performance.
Mrs. Bentley, born Phelps, was born in 1918 in the small coastal town of Waldport, Oregon.
Mrs. Bentley was an avid swimmer, camper and fisherman. The mother of five lived in the rural town of Molalla in northwest Oregon and grew vegetables for her large family until she died. The trained hairdresser also sang in her local church choir and taught Sunday school
The youngest of four, Mrs. Bentley, admitted that she was spoiled, according to her oldest child Patti Helmig, 78.
Mrs. Bentley was trained to become a hairdresser and volunteered as a nurse during WW2.
The & # 39; excellent swimmer & # 39; was very active and would often camp and fish her children, according to her third child Ginger Robbins, 76.
Mrs. Bentley – who lived in the rural town of Molalla in northwest Oregon – had her gallbladder, appendix and uterus removed during her lifetime.
Doctors, however, have never picked up her condition. But a surgeon noted that her appendix was in an unusual place in their notes.
She and her husband owned and operated the Bentley Food Store, which sold farm and pet supplies.
The couple visited all 50 states and traveled outside the US after they retired in 1980.
Until her death, Ms. Bentley attended the Molalla United Methodist Church, where she sang in a choir and taught Sunday School.
She was also an enthusiastic gardener and would grow vegetables to feed her large family.
Mrs. Bentley & # 39; s fourth child, Louise Allee, 66, added: & # 39; My mom would think this was so cool.
& # 39; She would turn pink, that she could learn something like that.
& # 39; She would probably get a big smile on her face, knowing that she was different, but she understood. & # 39;
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